Feasibility and Timing of Craniosynostosis Surgery in a Child with Hypoplastic Left Heart Syndrome

Holt-Oram Syndrome: A Rare Variant

Holt-Oram syndrome is an autosomal dominant disorder, characterised by skeletal abnormalities of the upper limb associated with congenital heart defect, mainly atrial and ventricular septal defects. Skeletal defects exclusively affect the upper limbs in the preaxial radial ray distribution and are bilateral and asymmetrical. They range from clinodactyly, absent or digitalised thumb, hypoplastic...

Anomalous origin of circumflex coronary artery from right pulmonary artery in a hypoplastic left heart syndrome child

We describe the case of a newborn with hypoplastic left heart syndrome (HLHS) and aberrant origin of the circumflex coronary artery from the right pulmonary artery. The patient underwent a modified Norwood procedure with direct reimplantation of the circumflex coronary artery to the neo-aorta, but died on the 5(th) postoperative day because of myocardial failure. Detailed assessment of coronary...

The Effect of Inhalation Anesthesia with Hyperventilation and Total Intravenous Anesthesia on Intracranial Pressure Control in Pediatrics with Craniosynostosis Surgery: A Randomized Clinical Trial

Background: Intracranial pressure (ICP) control is one of the anesthesiologist challenges in craniosynostosis repair surgery, especially in multiple sutures involvement. The aim of this study was comparing the effect of two anesthesia methods including inhalation with hyperventilation and total intravenous anesthesia (TIVA) on ICP control and surgeon satisfaction in pediatrics with craniosynost...

Right ventricular resynchronization in a child with hypoplastic left heart syndrome.

Hypoplastic left heart syndrome: parent support for early decision making.

Hypoplastic left heart syndrome is a life threatening congenital cardiac anomaly. After a child has been diagnosed with hypoplastic left heart syndrome, parents must make life or death decisions within days of birth. Healthcare providers must provide appropriate education so that parents are able to make informed, timely decisions. Information regarding the diagnosis, treatment options, and par...